Author index

  • HOME
  • BROWSE ARTICLES
  • Author index
Author     
Hyung Ro Moon  (Moon HR) 98 Articles
Case Report
Pena-Shokeir I Syndrome in a Newbonrn Infant
Myung Gil Han, Kyu Young Kim, Dong Woo Son, Bo Young Yoon, Kyung Hee Park, Do Hyun Kim, Hyung Ro Moon
Clin Exp Pediatr. 1997;40(5):721-725.   Published online May 15, 1997
Pena-Shokeir I syndrome is a multiple malformation syndrome displaying characteristics of camptodactyly, multiple ankylosis, severe muscle weakness, facial anomalies (low set ears, hypertelorism, depressed tip of nose), polyhydramnios, fetal growth retardation & pulmonary hypoplasia which are inherited by autosomal recessive trait. We experienced 1 case of Pena-Shokeir I syndrome in a neonate (41 weeks, 2.08Kg). This patient suffered from dyspnea. Respiratory...
Herditary Anhidrotic Ectodermal Dysplasiain Twins
Myung Gil Han, Do Hyun Kim, Hyung Ro Moon
Clin Exp Pediatr. 1996;39(7):1005-1009.   Published online July 15, 1996
Hereditary anhidrotic ectodermal Dysplasia is a congenital disease displaying characteristics of anhidrosis, hypotrichosis and dental defect which are caused by developmental anomaly of ectodermal epidermis and its appendages. We experienced two cases of hereditary anhidrotic ectodermal dysplasia in two-year and four-month old twin brothers. These patients suffered from intermittent high fever early in life which brought them to our clinical attention. However the diagnosis of...
A Case of Mauriac's syndrome
Se Young Kim, Choong Ho Shin, Il Soo Ha, Hae Il Cheong, Sei Won Yang, Yong Choi, Hyung Ro Moon
Clin Exp Pediatr. 1996;39(7):1020-1024.   Published online July 15, 1996
Mauriac's syndrome was described in the 1920s, as a triad of poorly controlled insulin dependent diabetes mellitus, profound growth retardation, and hepatomgaly. Following the wide availability of insulin and intensification of diabetic control, this entity has become quite rare. A 9-year-old female child was transferred to pediatric OPD of SNUCH because of hyperglycemia, short stature, and visual disturbance. Five years prior to admission, she...
Acanthosis Nigricans and TypeII Diabetes in Childhood
In Na Jeong, Hyung Ro Moon
Clin Exp Pediatr. 1996;39(3):404-410.   Published online March 15, 1996
The authors report two cases of type II diabetes with and without a acanthosis nigricans in children and a case of obese child with acanthosis nigricans encountered at Seoul Eul Ji Hospital in 1994 with review of literatures on relationship of obesity, acanthosis nigricans and type II diabetes. In case 1, 14-year old girl, BMI was 24 (weight, 63.5Kg ; height,...
Two Cases of Tetrahydrobiopterin Deficiency
Jee Won Choi, Sei Won Yang, Hyung Ro Moon, Se Chin Cho
Clin Exp Pediatr. 1995;38(3):397-403.   Published online March 15, 1995
Tetrahydrobiopterin(BH4) deficiency is a rare type of hyperphenylalaninemia and usually leads to a progressive neurologic deterioration despite early dietary control of blood phenylalanine concentration. We experienced two cases of BH4 deficiency in brother and sister, confirmed by biochemical study of blood and urine. They had suffered from a progressive neurologic illness such as mental retardation, severe hypotonia, seizure, and athetotic movements...
Original Article
Cushing Syndrome in Children and Adolescents
Choong Ho Shin, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1995;38(12):1677-1685.   Published online December 15, 1995
Purpose : Cushing syndrome occurs rarely in children and adolescents. The clinical manifestation is variable and growth is usually adversely affected. Methods : We retrospectively analyzed 8 patients with Cushing syndrome between the ages of 1 and 14 year who were admitted to the pediatric department of Seoul National University Children's Hospital during the period from 1978 to 1995. Results : 1)...
Pheochromocytoma in Children
Tae Sue Ha, Jae Hong Park, Il Soo Ha, Hae Il Cheong, Yong Choi, Hyung Ro Moon, Gui Won Park
Clin Exp Pediatr. 1994;37(7):961-968.   Published online July 15, 1994
We Reviewed 10 hypertensive children with pheochromocytoma retrospectively and the following results were obtained. 1) Out of 10 patients, 7 were male and 3 female. Age ranged from 5.5 years to 13.8 years and their median age was 9.9 years. 2) They complained of sweating, lethargy, headache, or chest pain and so on, Hypertension were noticed in all patients. Heart murmurs were...
The Correlation between the Bone Age and Predicted Adult height, Final Adult Height in the Children with Congenital Adrenal Hyperplasia, Especially 21-Hydroxylase Deficiency
Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1994;37(3):300-308.   Published online March 15, 1994
We studied the correlation between the bone age and the predicted adult height, final adult height in the 69 children (30 salt losing form and 39 non-salt losing form) diagnosed as 21-hydroxylase deficiency, retrospectively. The results were as belows; 1) The bone age was similar to the chronological age in the children with salt-losing form (5.3±3.5 years, respectively), but the bone age...
The Effect of Long-Acting Gonadotropin-Releasing Hormone (GnRH) Analog on the Growth Velocity and Final Adult Height in the Children with True Precocious Puberty
Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1994;37(3):309-316.   Published online March 15, 1994
The final adult height in the children with true precocious puberty are destined to be short due to excessive bone maturation, compared to the growth velocity, regardless of its etiologies. To improve this final shortness, long-acting GnRH analog have been tried to the children with true precocious puberty. We evaluated the parameters of the growth, including the growth velocity, height...
The Variability of Growth Hormone(GH) Response to Growth Hormone-Releasing Hormone(GHRH) according to the intrinsic Growth Hormone Secretory Rhythm in Children with Normal Growth Hormone Reserve
Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1993;36(3):312-319.   Published online March 15, 1993
The diagnostic value of GHRH in assenssing GH secretion in biochemical GH suficient short children was examined. GHRH(1㎍/kg i.v bolus) was given to three groups (upslope, trough, downslope) arbitrarily classified according to the basal pulsatile GH secretory pattern before GHRH administration. Cmax following GHRH administration were variable and overlapping. Two children in downslope group, three children in though group, and one...
Re-evaluation of TSH Screening TEST in Neonates
Jin Young Song, Dong Woo Son, Beyong Il Kim, Sei Won Yang, Jung-Hwan Choi, Chong Ku Yoon, Hyung Ro Moon
Clin Exp Pediatr. 1993;36(11):1502-1506.   Published online November 15, 1993
Five years ago, we made the cut-off value of TSH by dry filter paper method as 15μU/ml to screening congenital hypothyrodism. Since then, 1,210 term neonates, who had no perinatal problems, screening test with this cut-off point. Neonates had been recalled for measurement of serum T4/TSH to rule out congenital hypothyroidism if their TSH value by screening tests reveal more...
Standard of Ear Size in Korean Children
Heon Seok Han, Hyung Ro Moon
Clin Exp Pediatr. 1992;35(8):1089-1095.   Published online August 15, 1992
Measurement of 1298 Korean Children in Seoul (male 661; female 637) resulted in normal standard data for ear length and width by their age and sex. 1) Ear length and width were as follows respectively : 36.0¡¾2.5mm 21.5¡¾2.5mm in male neonate, 56.3¡¾3.1mm 30.6¡¾3.2mm at 6yr boy, 63.2¡¾3.5mm 33.4¡¾3.2mm in 14 yr adolescent male, 35.5¡¾2.0mm 21.2¡¾2.1mm in female neonate, 54.6¡¾3.1mm 28.7¡¾2.4mm in...
Case Report
A Case of Hypomelanosis of Ito Accompanying Turner Syndrome
Kyung Un No, Dong Wook Kim, Dong Joo Shin, Hyung Ro Moon
Clin Exp Pediatr. 1992;35(8):1157-1163.   Published online August 15, 1992
Hypomelanosis of Ito has been known to show the characteristic hypopigmentation of the skin over the trunk and the extremities following Blaschko lines, and to accompany abnormalities of the central nervous system, the skeletal system, the eye and so on. Lately, a variety of chromosomal anomalies, especially mosaicism, have been reported in association with hypomelanosis of Ito, which is believed...
A Case of WDHA(Watery Diarrhea Hypokalemia Achiorhydria) Syndrome
Nam Seon Beck, Jun Jai Kim, Beom Soo Park, Jeong Kee Seo, Hyo Seop Ahn, Hyung Ro Moon, Je Geun Chi
Clin Exp Pediatr. 1992;35(4):575-580.   Published online April 15, 1992
VIP secreting tumors are rare in children but they produce a dramatic clinical picture, the most prominent feature of which is profuse, watery diarrhea and hypokalemia. A 5-year-old girl was brought to Seoul National University Children's Hospital for evaluation of profuse watery diarrhea. She presented with watery diarrhea, hypokalemia, and stunted growth, and had experienced these problems for four years...
Original Article
Growth Promoting Effect of Recombinant methionyl-Growth Hormone in Children with Chronic Renal Failure
Heon Seok Han, Yong Choi, Hyung Ro Moon
Clin Exp Pediatr. 1992;35(10):1355-1360.   Published online October 15, 1992
The authors studied the growth-promoting effect of yeast-derived methionyl-hGH in short statured children with uremic chronic renal failure. The subjects were prepubertal chronic renal insufficient patients whose height standard deviation scores were below -2.0. Two boys and two girls participated in this study. Chronic renal insufficiency was the only cause for the short stature. HGH was given to the subjects in dose...
Clinical study on lipoid pneumonia caused by aspiration of squalene.
Dong Joo Shin, Beom Soo Park, Moon Sun Yang, Heon Seok Han, Young Yull Koh, Hyung Ro Moon, Chang Yeon Lee
Clin Exp Pediatr. 1991;34(5):654-661.   Published online May 31, 1991
A clinical observation was made on 14 cases of lipoid pneumonia, who visited department of pediatrics, Seoul National University Children’s Hospital from August, 1988 to June, 1990. The results were as follows; The ratio of male to female was 10 : 4. Age at diagnosis was 1.1±1. 3 years, and ranged from 3 months to 4.9 years. The age at taking Squalene ranged...
The etiologies and the clinical manifestations of hypoglycemia in infancy and childhood.
Nam Seon Beck, Dong Joo Shin, Heon Seok Han, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1991;34(4):480-486.   Published online April 30, 1991
To analysis age at onset, clinical manifestations, etiologies, complication and management of hypoglycemia, the authors reviewed seventeen cases of hypoglycemia who were admitted to Seoul National University Children’s Hospital because of hypoglycemic symtoms from March, 1982 to February, 1990. In neonate group, which included five patients, their initial symtoms were apnea, cyanosis, sweating and hand rigidity, with the causes of two hyperinsulinemic hypoglycemias, one...
A case of hypomelanosis of Ito accompanying ureteral duplication and hypomelanotic scalp hair.
Dong Woo Son, Beom Soo Park, Heon Seok Han, Hae Il Jung, Yong Choi, Hyung Ro Moon, Seon Hoon Kim, Hwang Choi
Clin Exp Pediatr. 1991;34(2):281-286.   Published online February 28, 1991
Hypomelanosis of Ito (incontinentia pigmenti achromians) is a cutaneous abnormality consisting of bizarre, whorly, linear, or patchy hypopigmentation over variable portion of body surface. Multiple assocaited defects in other systems occur in three quarters of the affected individuals. Most common- ly, the central nervous system, eye, and musculoskeletal structures are involved. It is suggested that the cutaneous abnormality, which is often detectable at birth...
Seventeen Years Experience on Inborn Errors of Metabolism A Study for Future Development of Inborn Errors of Metabolism in Korea.
Hong Jin Lee, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(8):1031-1036.   Published online August 31, 1990
In Korea, the study of inborn errors of metabolism is very primitive. Even the incidence and prevalence of the disease of inborn errors of metabolism are not known in Korea. We have done this study of inborn errors of metabolism in Korea and concluded that: 1) The varieties and incidences of inborn errors of metabolism in Korea might be relatively diverse and high. 2) Nation wide mandatory...
Four Cases of Attempted Suicide in Childhood.
Young Don Lee, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(5):666-670.   Published online May 31, 1990
Suicides and attempted suicides in childhood are not as rare as in commonly believed by foreign literatures. However a few cases of suicide in childhood were reported in Korea until the present or up to the present. A suicide attempt is usually interpreted as a cry for help and an indication of an individuafs frustration, distress and feelings of inadequacy to cope in some...
Three cases of Chronic Meningitis.
Soon Mee Park, In Sang Jeon, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(4):544-552.   Published online April 30, 1990
Chronic menigitis may be defined as symptoms and signs of meningeal inflammation lasting four weeks or longer. It has many infectious and noninfectious causes. Tuberculous and fungal infections are the most common causes. But no cause is found in the significant portions of chronic meningitis(idiopathic meningitis), although most appear to respond to treatment either with anti-tuberculosis drugs or steroids. Intereastingly eosinophilic pleocytosis in the cerebrospinal...
Pituitary Function on Patients with Sellar and Suprasellar Tumor.
Sei Won Yang, Hyung Ro Moon, Byung Kyu Cho
Clin Exp Pediatr. 1990;33(4):491-498.   Published online April 30, 1990
We observed the status of pituitary hormones (growth hormone, TSH, ACTH, gonadotropin and ADH) in the patients with intrasellar and suprasellar tumors (Table 1 and 2) before and after treatment of tumors. They were estimated from the results of various provocative tests to the pituitary hormones after confimation of normal thyroid function. The results were as belows (Table 3 and 4): 1) Most patients with craniopharyngioma...
Two cases of Goldenhar's Syndrome.
Ah Young Yun, Nam Sun Baik, Young Ah Lee, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(3):380-385.   Published online March 31, 1990
Goldenhar’s syndrome is a syndrome consisting of (1) epibulbar dermoids and/or lipodermoids (2) preauricular skin tags and blind-ended fistulas and (3) vertebral anomalies. Two cases of Goldenhar’s syndrome which showed asymmetric facies, epibubar dermoids, preaur- icular skin tags blind-ended fistulas in 7 month-old girl and 2 month-old boy were reported. In one of our cases cleft of vertebrae, hypoplasia of left lung and cyanotic...
Clinical Study of Mycoplasma Pneumoniae Infection in Children.
Jong Woon Choi, Hoan Jong Lee, Byung Kiu Park, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(3):315-323.   Published online March 31, 1990
A retrospective analysis of clinical findings in 43 patients with M. pneumoniae infection who visited Department of Pediatrics of Seoul National University Hospital from January, 1987 till December, 1987 was performed. 1) The peak incidence of age was 5 to 9 years of age (20 cases; 46.5%), and male-to-female ratio was 1.05:1. 2) Monthly distribution showed a high frequency in April (10 cases; 23.3%) and seasonal distribution showed...
Clinical Observation on isolated TRH deficient Congenital Hypothyroidism.
Heon Seok Han, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(10):1388-1393.   Published online October 31, 1990
Clinical features and endocrine function of 3 children with isolated TRH deficient congenital hypothyroidism followed at Seoul National University Children’s Hospital from Aug, 1986 to Aug. 1990 were reviewed. During above period 262 congenital hypothyroid patients were followed at endocrine clinic, number of congenital primary hypothyroidism was 218 cases (83.2%), and that of congenital secondary hypothyroidism was 44 cases (16.8%). Of the congenital primary hypothyroidism,...
A Clinical Study of Staphylococcus Aureus Infection in Children.
Yong Joon Shin, Young Pyo Chang, Dong Kyu Jin, Byung Kiu Park, Hoan Jong Lee, Hyung Ro Moon
Clin Exp Pediatr. 1990;33(1):35-41.   Published online January 31, 1990
We reviewed 113 patients with Staphylococcus aureus infection and 219 strains of Staphylococcus aureus isolated from pediatric patients of Seoul National University Hospital from Jan. 1, 1987 to Dec. 31, 1987. The results were as follows: 1) The proportion of MSSA was 50.2% of total Staphylococcus aureus isolated and that of MRSA was 49.8%. Staphylococcus aureus were isolated from pus (33.8%), urine (16.9%), ear discharge (8. 2%),...
Post-Exercise Pulmonary Function Changes in Asthmatic Children.
Kyung Ae Yoon, Young Yull Koh, Hyung Ro Moon
Clin Exp Pediatr. 1989;32(8):1074-1085.   Published online August 31, 1989
To determine the frequency, severity, time course and relations of exercise induced changes in lung function, forty-one asthmatic children and fifteen control children were subjected to free running and forced vital capacity (FVC), one-second forced expiratory volume (FEV1), maximum mid-expiratory flow rate (FEF 25-75%), and peak expiratory flow rate (PEFR) were measured before and serially for 60 minutes following exercise. The results were as follows. 1) Significant...
Late Infantile Metachromatic Leukodystrophy-Arylsulfatase A Assay in 24h Urine.
Hong Jin Lee, Yong Joon Shin, Yong Seung Hwang, Hyung Ro Moon, Jeong Seon Seo
Clin Exp Pediatr. 1989;32(7):978-983.   Published online July 31, 1989
A 2 year 5 month old female infant with late infantile metachromatic leukodystrophy was diagnosed by typical clinical and laboratory findings and Arylsulfatase A assay in 24h urine. The patient’s mother was confirmed as a heterozygote by Arylsulfatase A activities in 24h urine which was about one half of normal control groups.
Bone Age Determination and Hand Radiographic Findings in Children With Russell-Silver Syndrome.
Hun Kyu Lim, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1989;32(6):823-833.   Published online June 30, 1989
Russell.Silver syndrome is a disease of unknown etiology characterized by prenatal onset dwarfism irrespective of full term gestation, growth retardation, body asymmetry, craniofacial dysproportion with a triangular face, short and incurved little finger, etc. Forty.two children were diagnosed as Russell.Silver syndrome by Silver’s criteria at SNU Children' s Hospital from Apr. 1981 till Aug. 1988, and we reviewed clinical data and hand radiographs of...
A Case of Mixed Gonadal Dysgenesis.
Byung Ran Yun, Jae Il Sohn, Sei Won Yang, Hyung Ro Moon, Je Geun Chi
Clin Exp Pediatr. 1989;32(12):1757-1762.   Published online December 31, 1989
Mixed gonadal dysenesis is a disorder of sexual differentiation which is characterized by streak gonad associated with contralateral tesis, persistent Mullerian duct structures and/or sex chromosomal mosaicism most commonly with 45, X/46, XY. The authors experienced a case of mixed gonadal dysgensis in a 6-year old child who was reared as female and admitted due to clitoral enlargement. The patient had asymmetrical gonads consisted with...
Manometric Response to Heller's Myotomy in Achalasia.
Chun Wha Lee, Kyung Mo Kim, Jeong Kee Seo, Hyung Ro Moon, Joo Hyun Kim
Clin Exp Pediatr. 1989;32(1):101-108.   Published online January 31, 1989
Achalasia is an espohageal motility disorder. It is characterized by the loss LES relaxation on swallowing and of esophageal peristalsis and results in dysphagia, regurgitation and substernal pain. Manometry is one of several diagnostic tests of achalasia and reveals 1) Complete absence of esophageal peristalsis, 2) hypertension of LES. 3) impaired sphincter relaxation on swallowing and 4) positive esophageal body pressure compared to intragastric pressure. We...
Study on the Clitoral Size of the Korean Female Newborn.
Jong Lin Rhi, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1988;31(8):1007-1013.   Published online August 31, 1988
The disturbance of sex hormone secretions during the fetal life results in abnormal development of the fetal sex organs including the external genitalia. In the congenital adrenal hyperplasia, especially, the external genitalia is often virilized at birth and the clitomegaly in this disorder can be an important clue for the early diagnosis. For the normal range of the clitoral size of the Korean female...
Comparison of the Effects of Portacaval Shunt and Dietary therapy in Type I Gyocogen Storagy Diseases(GSD).
Dong Hyun Ju, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1988;31(6):762-771.   Published online June 30, 1988
Type I GSD is a metabolic disease resulted from defective glucose-6-phosphatase activities in liver, kindey and intestine. They are characterized by growth retardation, enlargement of liver and kidney, hypoglycemia, hyperuricemia, and hyperlipidemia. Various methods were suggested for the management of GSD. They are night-time nasogastric feeding of glucose solution with frequent day-time feeding, intravenous hyperalimentation, cornstarch therapy end-to-side portacaval shunt, etc. In this study, the effects...
Normal TSH Levels in Neonates by TSH Screening test.
Jae Won Song, Jong Lin Rhi, Sei Won Yang, Jung Hwan Choi, Chong Ku Yun, Hyung Ro Moon, Bo Youn Cho, Chang Soon Koh
Clin Exp Pediatr. 1988;31(6):754-761.   Published online June 30, 1988
In 110 term neonates without perinatal problems who were bom in SNUH, blood TSH levels were measured by TSH screening test for congenital hypothyroidism. The results are as follows 1) Normal TSH level was 14.8±7.8 µU/ml, 8.8±4.7 µU/ml, and 6.5±2.7 µU/ml in neonates of age 0 〜24 hours, 24—48 hours, and 48〜72 hours respectively, and all TSH values in neonates of age 48〜72 hours were...
A Case of Familial Dysautonomia.
Hong Jin Lee, Dong Kyu Jin, Sei Won Yang, Jeong Kee Seo, Hyung Ro Moon, Je Geun Chi
Clin Exp Pediatr. 1988;31(5):648-654.   Published online May 31, 1988
Few documented cases of Familial dysautonomia fulfilling current diagnostic criteria have been recognized in non-Jews especially in orientals. In our case diagnosis was established in 8 year old Korean girl. She fulfilled 8 out of 9 essential diagnostic criteria of Riley. It represents a report of this syndrome with achalasia and improved with modified Heller’s myotomy.
The Prevalence of Antithyroid Autoantibodies in Korean Children.
Bung Hai Ahn, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1988;31(3):329-338.   Published online March 31, 1988
The prevalence of antithyroid autoantibodies and the relationship between the presence of autoantibodies and thyroid functions were studied in 752 Korean children of 10 to 15 years of age with normal thyroids. Antimicrosomal antibodies (AMA) were measured by the indirect agglutination technique using artificial gelatin particle carriers sensitized with thyroid microsomal antigen and antithyroglobulin antibodies (ATA) by the tanned red cell hemagglutination technique. Circulating AMA...
Two Cases of Tsutsugamushi Disease in Children.
Eun Saing Jee, Hae Lim Chung, Hoan Jong Lee, Hyung Ro Moon
Clin Exp Pediatr. 1988;31(11):1509-1515.   Published online November 30, 1988
Tsutsugamushi disease is an acute infectious and febrile disease that is transmitted to human by larvae of several species of mites, Leptotrimbidium pallidum, Leptotrimbidium akamushi and Leptotrimbidium scutellare. Recently in Korea, this disease is increasingly reported in adult age but few cases are reported in pediatric age. We experienced two cases of tsutsugamushi disease in children, one of whom had no rash. This disease should be...
Study on the Korean Infant Development Screening Test.
Jong Lin Rhi, Jung Hwan Choi, Hyung Ro Moon, Sechin Cho
Clin Exp Pediatr. 1987;30(8):852-867.   Published online August 31, 1987
Developmental problems are relatively prevalent and often treatable if early interventions are to be given. Much better prognosis will also be given if they are treated early & properly by early detection through the use of the developmental screening test. Developmental screening is the application of relatively quick and simple procedures to an asymptomatic population to select out those individuals who are highly likely...
Case Report
A Case of Methylmalonic Acidemia.
Hyung Ro Moon, Hae Rim Jung, Mi Ryung Um
Clin Exp Pediatr. 1987;30(7):791-796.   Published online July 31, 1987
Methylmalonic acidemia is an inborn error of metabolsim, transmitted as an autosomal recessive traits. Symptoms begin early in life and they are pernicious vomiting, lethargy, hepatomegaly, and failure to thrive. Laboratory finidngs are ketosis, intermittent hyperglycinemia, and methymalonic aciduria without vitamin B12 deficiency. Six distinct subtypes of this disorders have been characterized. Some of them respond well to exogenous vitamin B12 therapy. We have experienced a...
A Case of Gaucher's Disease.
Hyo Nam Cho, Myung Cheol Cho, Hyung Ro Moon, Je Geun Chi, Hyo Min Kim
Clin Exp Pediatr. 1987;30(7):784-790.   Published online July 31, 1987
We experienced a case of Gaucher’s disease of acute infantile type in a 12 month old male boy. The patient showed hepatosplenomegaly with anemia and thrombocytopenia, developmental delay and frequent infection. There were characteristic Gaucher’s cells in bone marrow aspiration and biopsy of liver, spleen, & lymph node. Splenectomy was done at 25 month old. He expired 3 days after splenectomy. Autopsy was done....
Original Article
Clinical Approach to Dysmorphic Syndromes.
Hyung Ro Moon
Clin Exp Pediatr. 1987;30(7):707-711.   Published online July 31, 1987
A Clinical Observation on Fulminant Hepatitis in Children.
Hoan Jong Lee, Jeong Kee Seo, Hyung Ro Moon
Clin Exp Pediatr. 1987;30(4):406-415.   Published online April 30, 1987
Twenty-seven cases of fulminant hepatitis in children were retrospectively analyzed. The overall survival rate was 11%. The interval between onset of encephalopathy and death, and that between jaundice and death were 2-26 days (median 4 days), 4-61 days (median 14 days), respectively. HBs antigenemia was detected in 24%, HAV IgM was negative in 5 patients tested, and 4 cases were suspected as non-A, non-B...
A Cases of Dandy-Walker Syndrome.
Jong Lin Rhi, Yoon Dok Kim, Hyung Ro Moon
Clin Exp Pediatr. 1987;30(2):234-239.   Published online February 28, 1987
The Dandy-Walker syndrome is a developmental disorders of the brain characterized by cystic deformity of the fourth ventricle and agenesis or hypoplasia of the cerebellar vermis. Other systemic anomalies are associated with the syndrome. We experienced a case in a 15 day old female infant who presented initially with frequent aspirations and respiratory difficulty. On physical examination an encephalocele on the occipital area, a...
Pheochromocytoma in Two 10-year Old Children.
Young Soo Kim, Young Hoon Kim, Se Won Yang, Yong Choi, Hyung Ro Moon
Clin Exp Pediatr. 1987;30(2):207-211.   Published online February 28, 1987
We experienced two cases of pheochromocytoma in 10 year-old boy and girl. Boy had bilateral and girl had unilateral pheochromocytoma. Both patients who were severely retarded in height growth had hypertension and one patient had cardiomyopathy. In both patients, vanillylmandelic acid in urine was increased, and phentolamine test was positive. Adrenal mass was visualized by C.T. in each ease. Successful surgical removal was done,...
A Case of Type A Niemann Pick Disease.
Hyo Nam Cho, Hong Jin Lee, Jae Won Song, Jung Hwan Choi, Hyung Ro Moon, Je Geun Ji, Myeong Hee Park
Clin Exp Pediatr. 1987;30(12):1461-1467.   Published online December 31, 1987
We experienced a case of type A Niemann Pick disease in 13 month female baby. She showed marked hepatosplenomegaly, developmental regression and apathy. Fundoscopic examination revealed a cherry red spot in the macula. Numerous foamy histiocyte were seen in bone marrow. Autopsy finding revealed that liver, spleen, thymus, lymph node, lung and brain were involved. Liver showed fatty change. Generalized muscular atrophy and patch...
Russell-Silver Syndrome.
Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1986;29(7):715-722.   Published online July 31, 1986
Seventeen cases(12 boys and 4 girls) with Russell-Silver syndrome were evaluated for weight, height and bone age at initial presentation and during follow up. 1) Distribution of patient` s age at initial presentation was between 1 day and 75/12 year of age. 2) In 14 cases, the birth weight was below 3 percentile except for one case(3 percentile). In 15 cases, the...
Congenital adrenal Hyperplasia.
Byoung Hai Ahn, Sei Won Yang, Hyung Ro Moon
Clin Exp Pediatr. 1986;29(6):604-612.   Published online June 30, 1986
Clinical data of twenty-eight children with congenital adrenal hyperplasia who were admitted to the Seoul National University Hospital from June 1979 to July 1984 were analyzed retrospectively. Male to female ratio was 1 : 1.3. The average age at diagnosis was 3.2 years, 1.3 months for eleven salt-losers and all were 3 months or younger, 4.6 years for seventeen nonsaltlosers....
Case Report
Three Cases of Familial Glucocorticoid Deficiency.
Soo Heum Lim, Young Wun Kim, Byoung Hai Ahn, Hyung Ro Moon
Clin Exp Pediatr. 1986;29(5):549-552.   Published online May 31, 1986
Familial glucocorticoid defiency is a form of chronic adrenal insufficiency which is characterized by isolated deficiency of glucocorticoid and elevated levels of corticotropin in association with normal aldosterone production. It is thought to be degenerative process of adrenal cortex, with autosomal recessive or X-linked recessive pattern of inheritance. Skin hyperpigmentation and hypoglycemic symptom are characteristic and salt-losing symptom doesn’t develop....
A Case of the Dubowitz Syndrome.
Kyung Ae Lee, Chi Ho Yun, Jae Sun Jung, Hee Ju Kim, Sung Ill Ahn, Hyung Ro Moon
Clin Exp Pediatr. 1986;29(4):436-440.   Published online April 30, 1986
The Dubowitz syndrome is an autosomal recessive condition characterized by intrauterine growth retardation, postnanal growth retardation, peculiar facial appearance, short stature, low birth weight, microcephaly and borderline intelligence or mild mental retardation. We reported a typical case of the Dubowitz syndrome in a full term male infant together with a brief review of pertinent literatures since the incidence of the...
Two Cases of the Rud Syndrome in Siblings.
Mi Jeong Lee, Myung Geul Yum, Jung Hwan Choi, Chong Ku Yoon, Hyung Ro Moon
Clin Exp Pediatr. 1985;28(6):610-615.   Published online June 30, 1985
The Rud syndrome, which is characterized by ichthyosis, mental retardation, seizure, dwarfism, sexual infantilism, etc., was described by Rud in 1927 at first. It is hereditary disorder whose mode of inheritance is autosomal recessive. Because the incidence of this syndrome is very rare, the Rud syndrome has not been reported till now in Korea. We experienced two cases of the...
Hepatoblastoma with Rupture and Hemorrhage.
Kwang Wook Ko, Hyung Ro Moon, Je Geun Chi, Kwi Won Park
Clin Exp Pediatr. 1985;28(12):1261-1261.   Published online December 31, 1985
A Case of Niemann-Pick Disease with Sea-Blue histiocytes in the Bone Marrow.
Young Sun Kim, Soo Heum Lim, Jeong Kee Seo, Hyo Seop Ahn, Hyung Ro Moon
Clin Exp Pediatr. 1985;28(12):1238-1244.   Published online December 31, 1985
A case of Niemann-Pick disease in a 12 year and 6 month old Korean male was reported. The patient showed marked hepatosplenomegaly without neurologic symptoms. Fundoscopic examination revealed a cherry-red spot with white ring in the maculae. Numerous foamy histiocytes and sea-blue histiocytes were seen in the bone marrow. The liver biopsy specimen showed the diffuse ballooning of hepatocytes obliterating...
Two Case of Watson-Alagille Syndrome.
Heon Seok Han, Soo Heum Lim, Young Sun Kim, Jeong Kee Seo, Hyung Ro Moon
Clin Exp Pediatr. 1985;28(10):1047-1051.   Published online October 31, 1985
Watson-Alagille syndrome (Arteriohepatic dysplasia, Syndromatic paucity of interlobular bile duct), a disease characterized by chronic liver disease, characteristic facies, cardiova scular abnormalities, and vertebral arch abnormalities has paucity of interlobular bile ducts on histologic examination of liver. We experienced two cases of Watson-Alagille syndrome in a 7-month-old male infant and a 12-month-old male infant who had the chief complaint of...
Three Cases of Nephrogenic Diabetes Insipitus.
Hey Sun Lee, Byoung Hai Ahn, Jong Jin Seo, Hyung Ro Moon
Clin Exp Pediatr. 1984;27(9):912-917.   Published online September 30, 1984
From July 1981 to Feb. 1983, we experienced three cases of nephrogenic diabetes insipidus in which the initial diagnostic clues were repeated episodes of unexplained fever in infancy and which were confirmed by water deprivation and pitressin tests and clinical responses to administration of hydrochlorthiazide. So we report this with some review of literatures.
A Case of Glycogen Storage Disease Type IIa.
Dong Hyung Choo, Dong Kyoon Kim, Hyung Ro Moon, Choong Kon Kim
Clin Exp Pediatr. 1984;27(6):621-627.   Published online June 30, 1984
Glycogen storage disease type Ha(GSD la), also known as generalized glycogenosis, cardiomegalic glycogenosis, and Pompe disease, is a very rare form of glycogenosis. The authors reported a case of GSD J a in an eight months old girl who presented with respiratory problems, marked hypotonia, cardiomegaly, and macroglossia. The diagnosis was made on clinical grounds including pathologic findings of muscle...
Adrenal Cortical Carcinoma in a Nineteen Month Old Girl.
Sei Weon Yang, Jong Jin Seo, Hyung Ro Moon
Clin Exp Pediatr. 1984;27(4):413-418.   Published online April 30, 1984
Adrenal carcinoma is a rare disease both in adults and in children. Most of these tumors are functional, especially in children, producing endocrine syndromes such as Cushing syndrome, virilization, feminization or precocious puberty. The authors report a nineteen month old girl who exhibited features of Cushing syndrome and virilization caused by adrenal cortical carcinoma measuring 5.5X5.0X2.8 cm. She was successfully...
Hereditary Hemorrhagic Telangiectasia with Pulmonary Arteriovenous Fistula.
Heui Jeen Kim, Young Soo Yoon, Jeong Kee Seo, Hyung Ro Moon, Kyung Mo Yeon
Clin Exp Pediatr. 1984;27(4):390-394.   Published online April 30, 1984
Four Cases of Papillary Thyroid Cancer in Childhood.
Sei Weon Yang, Sei Won Park, In Sil Lee, Hyo Seup Ahn, Hyung Ro Moon, Chang Yee Hong, Kwi Won Park, Je Geun Chi
Clin Exp Pediatr. 1984;27(3):282-287.   Published online March 31, 1984
Papaillary thyroid cancer is a rare lesion in children. It progresses slowly and its prognosis is relatively good. A painless nodule in the thyroid or in the neck is the usual first evidence of disease. Cervical lymph node involvement is usually present at the time of the initial diagnosis and is often bilateral. The lungs are the most common site...
A Case of Treacher Collins Syndrome.
Hee Shang Youn, Koo Soo Kim, Hyung Ro Moon
Clin Exp Pediatr. 1984;27(2):207-212.   Published online February 28, 1984
The authors report a 5-year old boy who showed the abnormalities comprising relatively complete from of Treacher Colilns syndrome. These include hypoplasia of malar and mandibular bones, antimongoloid slant of palpebral fissures, colobomata of lower eyelids with defective eyelashes on medial sides, projection of scalp hair onto lateral cheeks, malformed auricles, complete atresia of both external auditory canals with defective...
Hypothyroid Myopathy.
Kawng Wook Ko, Je Geun Chi, Hyung Ro Moon
Clin Exp Pediatr. 1984;27(11):1147-1150.   Published online November 30, 1984
Acromesomelic Dysplasia Syndrome.
Hyung Ro Moon
Clin Exp Pediatr. 1984;27(1):98-104.   Published online January 31, 1984
A further case of acromesomelic dysplasia syndrome is reported in a twelve year old Korean boy born on January 15, 1971 at full term. His height was only 99.5 cm. on his visit to the outpatient department. The present case showed disproportionate shortening of the extremities, especially in the forearms, hands, shanks and feet together with most of the reported...
Original Article
Clinical Observation on Pediatric In-Patients Subjected for EEG.
Seung Kie Cheong, Hyung Ro Moon
Clin Exp Pediatr. 1983;26(9):891-898.   Published online September 30, 1983
This study include hundred and thirty-seven pediatric in-patients in whom EEG was performed at National Medical Center, from January, 1977 to Decmber, 1981. Clinical records and EEG of all subjects were analyzed and the following results were obtained. 1) The proportion of patients subjected to EEG ranged from 2.3 to 3.1 % (2. 6%) of total in-patients during five years of...
Observation on Chief Complaints of Pediatric Outpatients.
Sang Wook Choi, Hyung Ro Moon
Clin Exp Pediatr. 1983;26(9):843-849.   Published online September 30, 1983
Chief complaints of pediatric outpatients may reflect the patterns and severity of illnesses. As with the differences in prevalent illnessess in various periods of childhood, the chief complaints may also vary with age. This study was performed in order to investigate frequencies of various chief complaints in different age periods of childhood and rates of hospitalization for each chief complaint obtained at initial visit...
Clinical Observation on Tonsillectomy and Adenotosillectomy.
Joong Soo Park, Hyung Ro Moon
Clin Exp Pediatr. 1983;26(8):786-793.   Published online August 31, 1983
Clinical observations were made on the 1,040 cases of tonsillectomy and adenotonsillectomy and the medical records of 628 patients among 1,040 cases admitted to the Department of Otolaryngology, National Medical Center, Seoul from January 1971 to December 1980 for tonsillectomy and actenoidectomy. The following results were obtained. 1) The total number of tonsillectomy and adenotonsillectomy increased to 2. 6 times during the ten year period. The proportion...
Clinical Study on Cryptococcosis in Children.
Young Min Ahn, Hyung Ro Moon
Clin Exp Pediatr. 1983;26(4):315-327.   Published online April 30, 1983
The clinical aspects of childhood cryptococcosis were studied from ten patients admitted to the Pediatric ward of Seoul National University Hospital from January 1976 to December 1981 together with twenty-seven cases of childhood cryptococcosis reported in the Korean literatures. The following results were obtained. 1) The age was distributed between 1 4/12 and 13 5/12 years and males to females ratio was 1.3...
Statistical Assessment on Chromosomal Aberrations Observed in Childhood.
Jong Jin Seo, Hyung Ro Moon
Clin Exp Pediatr. 1983;26(3):220-227.   Published online March 31, 1983
A statistical assessment was carried out in two hundreds and eighty three inpatients and outpatients and fifteen mothers who were subjected to chromosomal analysis at Department of Pediatrics, Seoul National University Hospital, from January 1977 to February 1982. The following results were obtained: 1) Age distribution revealed 65.8% of all children subjected to chromosomal analysis to be: under 2 years of age. The number of...
Case Report
Pancreatic Pseudocysts and Ascites as Complications of Chronic Pancreatitis.
Nam Su Kim, Hee Ju Kim, Kyoo Duck Lee, Yong Choi, Hyung Ro Moon
Clin Exp Pediatr. 1982;25(2):183-189.   Published online February 28, 1982
A case of pancreatic pseudocysts and bloody pancreatic ascites as complications of chronic pancreatitis in eleven-year-old girl was reported. She was admitted to the pediatric ward with chief complaints of abdominal distension and bloody ascites. About nine months prior to admission, when she was stuck by a bicycle, she had sustained a blow on her abdomen. She has been apparently...
A Case of Congenital Hepatic Fibrosis.
Son Moon Shin, Sang Il Lee, Joong Gon Kim, Hyo Seop Ahn, Hyung Ro Moon, Kwang Wook Ko, Je Geun Chi
Clin Exp Pediatr. 1981;24(6):577-583.   Published online June 15, 1981
Congenital hepatic fibrosis is a relatively rare liver disease in children and young adults,that is characterized by stony hard hepatomegaly and portal hypertension with relative preservation of liver function and underlying architecture. Since this Condition was first delineated by Kerr et al in 1961, approximately over 150 cases have been reported in the literature. However, congenital hepatic fibrosis was not...
Original Article
Psychologic Disorders Among Pediatric Outpatients (Part I).
Hyung Ro Moon
Clin Exp Pediatr. 1981;24(5):477-484.   Published online May 15, 1981
One hundred and twenty-seven children with psychologic problems were encountered by the author at twice weekly morning walk-in clinics of the pediatric department of Seoul National University Hospital during the nine months period from January through September 1980. Diagnostic clues for psychogenic origin of various somatic complaints were obtained from complete history taking, thorough physical examination, tests and laboratory procedures...
Clinical Assessment on Wilson's Disease.
In Sil Lee, Young Yul Koh, Hyung Ro Moon
Clin Exp Pediatr. 1981;24(12):1165-1172.   Published online December 15, 1981
The clinical and laboratory manifestations in ten children with Wilson* s disease are described. The average at onset of symptoms in the eight symptomatic patients was ten years, and male to female ratio was 6 to 4. Kayser-Fleisher rings were present in eight patients. Splenomegaly and hepatomegaly were noted in. four patients and generalized edema was present in six patients. Less...
Case Report
Two Cases of the Salts Losing Congenital Adrenal Hyperplasia.
Hee Ju Kim, Hyung Ro Moon
Clin Exp Pediatr. 1981;24(11):1092-1099.   Published online November 15, 1981
The authers experienced two cases of salt losing congenital adrenal hyperplasia. Case I was a 100 day old male infant, who had dehydration, failure to thrive, and diffusely pigmented skin. Very low plasma aldosterone and markedly increased urinary 17KS were observed. He had been, treated with daily DOCA injection and oral hydrocortisone, successfully. Case H was a 5 year and...
Original Article
The Relationship between hand and foot Length and Other Anthropometric Measurements in Neonates.
Hee Ju Kim, Hyung Ro Moon
Clin Exp Pediatr. 1980;23(7):511-520.   Published online July 15, 1980
The hand length, foot length, middle finger length as percentage of total hand length, palm length, height, birth weight head circumference of 143 neonates of gestational ages ranging from twen-five to fourty-two weeks were measured between 12 hours and 5 days of life in order to find out normal values and correation between them. The subjects were devided into three...
Case Report
2 Cases of Cushing's Syndrome.
Whan Jong Lee, Kwang Chan Do, Hyung Ro Moon, Woo Ki Kim, Yong Il Kim
Clin Exp Pediatr. 1980;23(4):326-336.   Published online April 15, 1980
Cushing's syndrome is a rare entity in pediatric age, and and mostly caused by adrenocotical tumor. We recently experiecd 2 cases of Cushing's syndrome, one, 13 year and 4 month old girl with bilateral adrenocortical hyperplasia, and one, 2 year and 4 month old girl with huge adrenocortical carcinoma measuring 14x13x8cm, thought to be congenital in origen. The former was...
Original Article
Statistical Study on Visually Handicapped Children.
Ki Young Lee, Kyung Tai Whang, Sang Woo Kim, Soo Woong Lee, Young Sil Rhee, Hyung Ro Moon
Clin Exp Pediatr. 1980;23(4):269-279.   Published online April 15, 1980
A statistical study on visually handicapped children was performed by The Committee on Health of Korean Pediatric Association from July to October, 1978. 3,930 boys and girls in middle school children(3rd grade; around 15 years of age) were studied and the results were obtained as follows; 1, 788 out of 3,930 children(20.1%) were visually handicapped. There were no sex preponderance....
Case Report
A Case of Chylous Ascites in an Infant Boy.
Kyu Chan Kim, Hae Il Cheong, Yong Choi, Hyung Ro Moon
Clin Exp Pediatr. 1980;23(1):63-67.   Published online January 15, 1980
The authors report a case of chylous ascites in a two month old boy with massive ascites. He was managed with repeated therapeutic paracentesis and skimmed milk feeding. A marked improvement was resulted in clinical symptoms and laboratory findings at the time of discharge to be followed-up at the outpatient service. A brief review of literatures is included
Gentamicin-resistant Pseudonomas Aeruginosa Menigitis.
Chung Il Noh, Yong Soo Yoon, Hyung Ro Moon, Chang Yee Hong
Clin Exp Pediatr. 1979;22(7):525-531.   Published online July 15, 1979
We have treated 4-year-old with amikacin and rifampin, who suffered from bacterial meningitis due to gentamicin-resistant Pseudomonas aeruginosa. There was no complication during treatment. Even though we didint check audiometry and BUN and/or creatinine, urinalysis was normal and physical examination revealed no abnormalities. He had been treated fora about 3 months with various antibiotics including gentamicin, intravascular and intrathecal, and...
Original Article
Statistical study on physically and Mentally Handicaped Children.
Ki Young Lee, Kying Tai Whang, Sang Woo Kim, Young Sil Rhee, Soo Woong Lee, Hyung Ro Moon
Clin Exp Pediatr. 1978;21(9):556-567.   Published online September 30, 1978
A study on physically and mentally handicaped children was carried out by health commttee of korean pediatric Association on August, 1977. 654 children in 5 special children's Institutes in Seoul area were observed and the results obtained were as follows ; 1. 393 out of 654 cases were males and male to female ratio was 6 : 4. The most...
Case Report
Two cases of Cryptococcosis in Children.
Chuny Hang Park, Youg Soo Yoon, Hyung Ro Moon, Han Woong Choi
Clin Exp Pediatr. 1978;21(3):225-231.   Published online March 31, 1978
Cryptococcosis is a subacute or chronic mycotic infection caused by cryptococcus neoformans with a special predilection for the lung, skin and central nervous system, but rarely involving the lymphatic system. Recently the authors have experienced two patients with cryptococcosis in volving the liver and lymph nodes. One was 31/4year old male and the other was 11 year old male. The...
Original Article
Height and weight (and other measurements) of children in Korea 1975.
Hyung Ro Moon, Duk Jin Yun
Clin Exp Pediatr. 1978;21(3):183-197.   Published online March 31, 1978
Clinical observation on subacute bacterial endocarditis with emphasis on pulmonary perfusion scan in the diagnosis of pulmonary infarction.
Byong Kwan Son, Hyung Ro Moon
Clin Exp Pediatr. 1978;21(12):1110-1115.   Published online December 31, 1978
Total thirteen cases of subacute bacterial endocarditis were seen at the Department of Pediatrics, Seoul National University hospital from January 1971 to September 1978. Among them, twelve patients' medical records were analyzed for clinical data and particular attention was given on the usefulness of pulmonary perfusion scan in the diagnosis of pulmonary infarction, which is the one of the frequent...
The Incidence of Genetic Disease among Pediatric in-patients in a University Hospital.
Hyung Ro Moon
Clin Exp Pediatr. 1977;20(2):100-105.   Published online February 28, 1977
The frequency of genetic disease among in-patients of Pediatric department, Seoul National University Hospital during two-year period from January 1972 to December 1973 was surveyed. A total of 1,413 admission records which included all but two-hundred sixteen patients whose records failed to specify primary diagnosis were subjected for present study. Primary diagnoses were classified into following seven categories: single-gene disorders,...
Case Report
A Case of Collodion Baby.
Baek Youn Choo, Hyung Ro Moon
Clin Exp Pediatr. 1977;20(11):907-910.   Published online November 30, 1977
A typical case of collodion baby was reported. On admission, the entire skin surface of this infant was covered with collodion-like membrane with fissures and exfoliations. Flexion contracture of all four extrimities and ectropion of both eyes were also appeared on admission. The family history and laboratory findings were unremarkable. The skin lesions were almost completely healed after application of...
A Case Report of Localized Scleroderma.
Ho Sung Lee, Hyung Ro Moon
Clin Exp Pediatr. 1977;20(11):902-906.   Published online November 30, 1977
The authors report a case of localized scleroderma in a 7-year-old girl. Three years prior to admission, she became aware of a small depressed patch in the right inguinal region. The lesion gradually enlarged by linear extension superiorly toward the lower abdomen and inferiorly to the external genitalia. Two years later, the original lesion extended to the left side of...
DiGeorge Syndrome
Tae Woon Kim, Yong Choi, Hyung Ro Moon
Clin Exp Pediatr. 1976;19(5):366-371.   Published online May 31, 1976
A case of DiGeorge syndrome in 2-month-old male infant was presented with a brief review of literature. He was characterized by a malformed right ear, a short philtrum of the upper lip, polydactyly, hypocalcemia, generalized, convulsions and absence of the thymic shadow in a film of the chest. Although the generalized convulsions were abated with calcium gluconate therapy, he died on...
Original Article
Some Prevalent Medical Problems of Children in Doctorless Area(Effectiveness of mobile medical team activities)
Hyung Ro Moon
Clin Exp Pediatr. 1975;18(4):300-308.   Published online April 30, 1975
A survey was carried out on some prevalent medical problems of children living in a doctorless area during the period of July 26 to July 29, 1973. Total two-hundred eighty-eight children among four-hundred fourty-two children who attended a mobile medical team organized by the Student Body of College of Medrcine, Seoul National University were observed for age, sex, chief complaints,...
Detection of Sex of Fetuses
Hyung Ro Moon
Clin Exp Pediatr. 1974;17(7):482-489.   Published online July 31, 1974
The over-all accuracy and reliability of prenatal sex determination by sex chromatin analysis in 739 samples of uncultured amniotic fluid cells were 97%(88〜 100%) and 82% (59〜 100%), respactively. The wide ranges in accuracy and reliability were influenced by variations in gestation period at amniocentseis, amount of fluid aspirated, number of cells counted, staining method used, and incidence of sex chromatin positive cells...
Total Ridge Counts in Normal Korean Males and Females
Hyung Ro Moon
Clin Exp Pediatr. 1974;17(3):194-200.   Published online March 31, 1974
Total ridge counts in normal Korean males and Jemales as well as individuals with sex-chro- mosomal aberrations were reported in this study. The mean total ridge count (TRC) in three hundreds and twenty-five school boys and too hundreds and eighty-nine school girls was 146±40. 2 S.D. (range, 88-208) and 132. 2±48.5 S.D.(range 74-203), respectively. The examinations of finger-tip pattern types, ridge counts and...
Incidence of Unusual Dermatoglyphics in Normal Korean Children
Hyung Ro Moon
Clin Exp Pediatr. 1973;16(5):368-375.   Published online May 31, 1973
An analysis of dermatoglyphics in normal Korean children was undertaken in order to survey the incidence of unusual dermal patterns. The results of direct observation of dermal patterns of each subject were tabulated, and percentage frequencies of each unusual dermal pattern and combinations of patterns were obtained.
Case Report
A Case of Total Anomalous Pulmonary Venous Return
Hyo Seop Ahn, Soon Young Kim, Tae Woon Kim, Jong Ku Yoon, Hyung Ro Moon, Chang Yee Hong, Hye Soon Chang, Man Cheong Han
Clin Exp Pediatr. 1973;16(2):156-160.   Published online February 28, 1973
A case of total anomalous pulmonary venous return in a 10 year and 8 month-old female was presented. The patient was admitted with the chief complaints. of palpitation and growth retardation. The diagnosis was confirmed by right heart catheterization and angiocardiography. The review of literature was made briefly.
Original Article
Frequency of Neonatal Physiologic Jaundice
Hyung Ro Moon
Clin Exp Pediatr. 1971;14(5):275-280.   Published online May 31, 1971
Frequency of neonatal physiologic jaundice was investigated retrospectively through discharge summary notes of the newborn nursery of Seoul National University Hospital between May 1970 :and October 1970. The total number of infants included in the present study was 599. 1)The incidence of neonatal physiologic jaundice in this series was 47. 9% which probably represents less than true incidence since there...
Cytogentic Survey of Children with Mental Retardation
Hyung Ro Moon
Clin Exp Pediatr. 1970;13(6):337-344.   Published online June 30, 1970
Seven children with Down’s syndrome, five boys and two girls, were included to cytogenetic survey. All of the children were clinically diagnosed by the presence of various combinations of microsymptoms or stigmata frequently observed in Down’s syndrome. To supply additional evidence for the diagnosis, data on the direct observation of dermatoglyphic patterns were also recorded. Chromosomal analyses revealed diploid number...
Case Report
Two Cases of Congenital Adrenogenital Syndrome
Yung Cho Kwon, Chong Koo Yun, Chang Soo Rha, Hyung Ro Moon, Byung Hee Lee
Clin Exp Pediatr. 1969;12(4):205-212.   Published online April 30, 1969
The authors report two cases of congenital adrenogenital syndome. The patient in case I was a girl born with ambiguious sex, and manifested virilization and accelerated growth. The height and bone age on admission at age of 3 years and 10 mounths was 103. 5 cm. and 6 years and 9 months, respectively. The vaginogram revealed normal internal genital organs....
Salmonella Osteomyelitis
G.W. Ahn, Sang Kook Lee, S.I Chin, Choo Wan Kim, Byung Hoon Rie, D.H Ahn, Hyung Ro Moon
Clin Exp Pediatr. 1969;12(3):159-164.   Published online March 31, 1969
A case of salmonella osteomyelitis in a 2 year old boy was reported. As far as we know, this is the first reported case in korea. The diagnosis was confirmed by widal test, bacterial cultures of pus from periosteal collection and maculopapular pustules on the face and left wrist, radiological studies of the bones. The autopsy findings were presented. Review of literatures was...
Original Article
Detection of Tuberculin Sensitivity by Leukocyte Culture
Hyung Ro Moon
Clin Exp Pediatr. 1969;12(12):669-674.   Published online December 31, 1969
Blood specimens obtained from 15 children with positive and negative Mantoux reaction were incubated with OT, PHA-M (as a positive control) and without reagent (as a negative control) in three culture vials using leukocyte culture technique. The following results are obtained. The Mantoux-positive inactive tuberculous group showed marked lymphocytic blastogenesis including mitotic figures when cultured with OT. On the other...
Case Report
A Case of Stevens-Johnson Syndrome (Erythema Multiform Exudativum)
Yong Ae Lee, Byung Hi Lee, Hyung Ro Moon
Clin Exp Pediatr. 1968;11(7):371-374.   Published online July 31, 1968
This report presents a case of Stevens-Johnson syndrome in a 7 year old boy. The patient was admitted with chief complains of high fever, dyspnea, cough, abdominal pain, headache, generalized skin eruption after administration of sulfadiazine fcr a period, of 7 days for treatment of pneumonia by a local physician. The diagnosis of Stevens-Johnson syndrome was established by history, clinical symptoms, physical findings and prognosis.
A Case of Cushing's Syndrome in the Childhood
Soon Yong Lee, Nam Je Im, Hyung Ro Moon, Myung Ha Cho, Pyung Chui Min
Clin Exp Pediatr. 1968;11(3):137-142.   Published online March 31, 1968
This report presents a case of Cushing’s syndrome in childhood. The 13 years-old female patient was admitted with the complaints of headache, moon face, obesity and hirsuitism, and was diagnosed as Cushing’s syndrome due to adrenocortical carcinoma of the left adrenal gland. Complete resection of the tumor was successfully done- After operation, her clinical course was markedly improved.
Original Article
Frequency of Drumsticks in Neutrophils of Infants and Older Children
Hyung Ro Moon
Clin Exp Pediatr. 1967;10(4):195-204.   Published online April 30, 1967
The occurence of the drumsticks in neutrophils was studied in ninety females including fourty newborn infants, thirty older children and twenty young women; the latter serving as a control group. Thirty-six boys including thirty-one newborn infants of comparable ages to those of the opposite sex were also subjected for the same purpose. The follwing results are obtained: 1.The incidence of...
Influence of The Central Nervous System on Changes in Urine Volume
Hyung Ro Moon
Clin Exp Pediatr. 1962;5(2):103-128.   Published online April 30, 1962
There have been a number of experimental studies mcerning role of the central nervous sytem in metallism of electrolytes and water since Bernard first iscovered diuresis in the absence of glycosuria by metrating a cetain part of floor of the fourth ventricle. Nevertheless, not until present were definite studies jrformed which indicated the limbic system is integral the neural control...
  • PubMed Central
  • PubMed
  • Scopus
  • Directory of Open Access Journals (DOAJ)